https://www.askep3s.org/a304443b60/pathway/E71.0
ICD-10: E71.0
19 Node
18 Relasi
E71.0 Maple Syrup Urine Disease
Clinical Pathway interaktif: Etiologi → Patofisiologi → Dx Keperawatan
Patofisiologi10
- Defisiensi Enzim BCKD
- Akumulasi Leucine
- Ensefalopati Metabolik
- Edema Serebral
- Hipoksia Serebral
- Ketoasidosis Metabolik
- Hipoglikemia
- Dehidrasi
- Neurotoksisitas Kronis
- Imunosupresi
Diagnosis Keperawatan7
- D.0019 Defisit Nutrisi
- D.0066 Penurunan Kapasitas Adaptif Intrakranial
- D.0064 Konfusi Akut
- D.0027 Ketidakstabilan Kadar Glukosa Darah
- D.0023 Hipovolemia
- D.0107 Risiko Gangguan Perkembangan
- D.0142 Risiko Infeksi
Referensi & Sumber
- Kemenkes RI. (2020). Standar Diagnosis Keperawatan Indonesia (SDKI).
- PPNI. (2017). Standar Layanan Keperawatan Profesional Indonesia.
- Nelson, W.E., et al. (2019). Buku Ajar Pediatri Nelson (Indonesian Edition).
- Saudubray, J.M., et al. (2016). Inborn Metabolic Diseases: Diagnosis and Treatment.